Nevus comedonicus with hidradenoma papilliferum and syringocystadenoma papilliferum in the female genital area

Background: Nevus comedonicus is an uncommon malformation of the pilosebaceous unit. Association of nevus comedonicus with tumors originating from the apocrine gland has not previously been reported. Method: We present a case of nevus comedonicus associated with hidradenoma papilliferum (HAP) and syringocystadenoma papilliferum (SCAP) in the female genital area. Results: Histological features strongly suggested nevus comedonicus associated with HAP and SCAP. Conclusion: Although the association of nevus comedonicus with HAP and SCAP is very rare, the possibility of coexistence cannot be excluded.